Adult Pulmonary Langerhans Cell Histiocytosis: a National Registry-based Prospective Cohort Study
Adult Pulmonary Langerhans Cell Histiocytosis: a National Registry-based Prospective Cohort Study
The long-term outcomes of adult patients with pulmonary Langerhans cell histiocytosis (PLCH),
 particularly survival, is largely unknown. This is the first prospective study in the field
 evaluating the long-term outcomes of PLCH patients. This french countrywide registry-based
 study included a large cohort of PLCH patients followed for a sufficiently long period to
 address risk factors of long-term outcomes of PLCH patients.
Inclusion Criteria:

 -  Age >= 18 years

 -  Diagnosis of PLCH was either histologically confirmed on a biopsy of an involved
 tissue, or based on the combination of the following criteria: 1) an appropriate
 clinical picture; 2) a typical nodulo-cystic pattern on lung high-resolution computed
 tomography (HRCT) and 3) exclusion of alternative diagnoses

 Exclusion Criteria:

 -