RaDiCo PID Cohort (RaDiCo-ILD Cohort in English)
RaDiCo PID Cohort (RaDiCo-ILD Cohort in English)
The main objective is to describe the phenotypic features of the paediatric and adult
 patients with Idiopathic Interstitial Pneumopathy/Pneumopathy Interstitial Diffuse (IIP/PID),
 at diagnosis and during the follow-up. These data will be critical for the description of the
 natural history of the various forms of IIP/PID.
The French RaDiCo-PID : Idiopathic Interstitial Pneumopathy registry is an ongoing
 observational prospective and retrospective cohort with longitudinal long-term follow-up
 includes pediatric and adult patients with Idiopathic Interstitial Lung Disease (ILD) from
 the reference and competence centers.
Inclusion Criteria:

 -  Clinical criteria: chronic respiratory insufficiency manifestations including
 dyspnea/tachypnea, cough, and cyanosis during exercise or at rest

 -  Radiological criteria: characteristic chest High-Resolution Computed Tomography (HRCT)
 abnormalities including widespread ground glass or alveolar attenuation, reticulation
 often associated with traction bronchiectasis, and honeycombing

 -  Functional criteria: pulmonary function test abnormalities reflecting a restrictive
 pattern and including: loss of lung volume, vital capacity (VC), total lung capacity
 (TLC); reduction in the diffusion capacity of the lung for carbon monoxide (DLCO), gas
 exchange abnormalities, and altered ventilatory response to exercise

 -  Patients (parents/guardians for paediatric/patients) having given an informed consent
 to participate in the protocol

 -  Patients affiliated to the "Regime National d'Assurance Maladie"

 Exclusion Criteria:

 -  Patients with diffuse parenchymal lung diseases caused by drug toxicity,
 immunodeficiency, proliferative disorders including histiocytosis, and metabolic
 disorders

 -  Patients (parents/guardians for paediatric patient) not able to approve/understand the
 protocol